Rétinoblastome

A B C D E F G H I K L M N O P R S T U V X Z

Rétinoblastome

Synonyme(s) - Gliome de la rétine - Gliome rétinien - Neuroblastome rétinien - Rétinoblastome héréditaire - Rétinoblastome familial

Définition: A malignant tumor arising from the nuclear layer of the retina that is the most common primary tumor of the eye in children. The tumor tends to occur in early childhood or infancy and may be present at birth. The majority are sporadic, but the condition may be transmitted as an autosomal dominant trait. Histologic features include dense cellularity, small round polygonal cells, and areas of calcification and necrosis. An abnormal pupil reflex (leukokoria); NYSTAGMUS; STRABISMUS; and visual loss represent common clinical characteristics of this condition. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2104)

Classification hiérarchique

  • Tumeurs
  • Tumeurs par type histologique
  • Tumeurs embryonnaires et germinales
  • Tumeurs neuroectodermiques
  • Tumeurs neuroépitheliales
  • Rétinoblastome

Consultez aussi notre page sur ce sujet

 

MeSH © U.S. National Library of Medicine (NLM)®
MeSH © Equipe "Centre Medlars" du réseau DIC-DOC de l'INSERM (version française)
Définitions Professionnelles © HON

Chercher dans Pro Visu